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DeCS
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Descritor Inglês:
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Isolated Noncompaction of the Ventricular Myocardium
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Descritor Espanhol:
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No Compactación Aislada del Miocardio Ventricular
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Descritor Português:
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Miocárdio Ventricular não Compactado Isolado
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Sinônimos Inglês:
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Isolated Non-compaction of the Ventricular Myocardium
Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked
Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
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Categoria:
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C14.240.400.660
C14.280.238.281.500
C14.280.400.660
C16.131.077.477
C16.131.240.400.655
C16.320.322.370
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Definição Inglês:
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Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen. |
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Nota Histórica Inglês:
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2010
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Qualificadores Permitidos Inglês:
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Número do Registro:
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53536
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Identificador Único:
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D056830
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Ocorrência na BVS:
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Similar:
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DeCS
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